Papillary Tumor of the Pineal Region in a Child – a Case Report

Czech version

Authors: Z. Pavelka ¹; M. Smrčka ²; L. Křen ³; M. Keřkovský ⁴; J. Skotáková ⁵; P. Šlampa ⁶; K. Zitterbart ¹; J. Štěrba ¹
Authors‘ workplace: Klinika dětské onkologie LF MU a FN Brno ¹; Neurochirurgická klinika LF MU a FN Brno ²; Ústav patologie LF MU a FN Brno ³; Radiologická klinika LF MU a FN Brno ⁴; Klinika dětské radiologie LF MU a FN Brno ⁵; Klinika radiační onkologie LF MU a MOÚ v Brně ⁶
Published in: Cesk Slov Neurol N 2012; 75/108(6): 754-756
Category: Case Report

Overview

We describe a case of a five years old girl with a large tumor of the pineal region, the 3^rd and 4^th ventricles, presented with the increased intracranial pressure syndrome. Endoscopic third ventriculostomy with tumor biopsy was performed, and the tumor was classified as papillary tumor of the pineal region. Local relapse occurred fourteen months after complete resection and it was treated with stereotactic external fractionated radiotherapy. Papillary tumor of the pineal region is a rare tumor with a difficult diagnosis, uncertain prognosis, and a high risk of local recurrence. The only defined prognostic factor is radicality of the resection. Most adult patients are treated with a combination of surgery and adjuvant local radiotherapy. A standard of care for children has not been clearly defined yet.

Key words:
papillary tumor – pineal region – radiotherapy – chemotherapy

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